[Stewart-Treves syndrome (angiosarcoma on lyphoedema): A rare complication of lymphoedema].
Identifieur interne : 000319 ( France/Analysis ); précédent : 000318; suivant : 000320[Stewart-Treves syndrome (angiosarcoma on lyphoedema): A rare complication of lymphoedema].
Auteurs : Eva Wierzbicka-Hainaut [France] ; Gérard GuilletSource :
- Presse medicale (Paris, France : 1983) [ 2213-0276 ] ; 2010.
Descripteurs français
- KwdFr :
- Association thérapeutique, Complications postopératoires (diagnostic), Complications postopératoires (mortalité), Complications postopératoires (étiologie), Femelle, Humains, Hémangiosarcome (), Hémangiosarcome (diagnostic), Hémangiosarcome (mortalité), Hémangiosarcome (étiologie), Lymphangiosarcome (), Lymphangiosarcome (diagnostic), Lymphangiosarcome (mortalité), Lymphangiosarcome (étiologie), Lymphoedème (), Lymphoedème (diagnostic), Lymphoedème (mortalité), Maladie chronique, Mastectomie radicale, Pronostic, Taux de survie, Tumeurs du sein (), Tumeurs du sein (mortalité).
- MESH :
- diagnostic : Complications postopératoires, Hémangiosarcome, Lymphangiosarcome, Lymphoedème.
- mortalité : Complications postopératoires, Hémangiosarcome, Lymphangiosarcome, Lymphoedème, Tumeurs du sein.
- étiologie : Complications postopératoires, Hémangiosarcome, Lymphangiosarcome.
- Association thérapeutique, Femelle, Humains, Hémangiosarcome, Lymphangiosarcome, Lymphoedème, Maladie chronique, Mastectomie radicale, Pronostic, Taux de survie, Tumeurs du sein.
English descriptors
- KwdEn :
- Breast Neoplasms (mortality), Breast Neoplasms (surgery), Chronic Disease, Combined Modality Therapy, Female, Hemangiosarcoma (diagnosis), Hemangiosarcoma (etiology), Hemangiosarcoma (mortality), Hemangiosarcoma (therapy), Humans, Lymphangiosarcoma (diagnosis), Lymphangiosarcoma (etiology), Lymphangiosarcoma (mortality), Lymphangiosarcoma (therapy), Lymphedema (complications), Lymphedema (diagnosis), Lymphedema (mortality), Mastectomy, Radical, Postoperative Complications (diagnosis), Postoperative Complications (etiology), Postoperative Complications (mortality), Prognosis, Survival Rate.
- MESH :
- complications : Lymphedema.
- diagnosis : Hemangiosarcoma, Lymphangiosarcoma, Lymphedema, Postoperative Complications.
- etiology : Hemangiosarcoma, Lymphangiosarcoma, Postoperative Complications.
- mortality : Breast Neoplasms, Hemangiosarcoma, Lymphangiosarcoma, Lymphedema, Postoperative Complications.
- surgery : Breast Neoplasms.
- therapy : Hemangiosarcoma, Lymphangiosarcoma.
- Chronic Disease, Combined Modality Therapy, Female, Humans, Mastectomy, Radical, Prognosis, Survival Rate.
Abstract
Stewart-Treves syndrome (SST) or former lymphangiosarcoma is a rare complication of chronic lymphoedema mainly related to the breast cancer (90% of cases). It occurs in 0.03% of patients surviving 10 or more years after radical mastectomy. The prognosis is very poor with a five-year survival close to 10% despite the various treatment modalities. The treatment of choice is a large resection, but some authors recommend radical resection in the form of shoulder disarticulation or forequarter amputation. Surgical treatment can be preceded or followed by radiation therapy. Locally advanced tumors or metastatic forms can be treated with mono or polychemotherapy, systemic or local.
DOI: 10.1016/j.lpm.2010.06.017
PubMed: 20970956
Affiliations:
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pubmed:20970956Le document en format XML
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<term>Breast Neoplasms (surgery)</term>
<term>Chronic Disease</term>
<term>Combined Modality Therapy</term>
<term>Female</term>
<term>Hemangiosarcoma (diagnosis)</term>
<term>Hemangiosarcoma (etiology)</term>
<term>Hemangiosarcoma (mortality)</term>
<term>Hemangiosarcoma (therapy)</term>
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<term>Lymphangiosarcoma (etiology)</term>
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<term>Lymphangiosarcoma (therapy)</term>
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<term>Lymphedema (mortality)</term>
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<term>Postoperative Complications (etiology)</term>
<term>Postoperative Complications (mortality)</term>
<term>Prognosis</term>
<term>Survival Rate</term>
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<term>Complications postopératoires (diagnostic)</term>
<term>Complications postopératoires (mortalité)</term>
<term>Complications postopératoires (étiologie)</term>
<term>Femelle</term>
<term>Humains</term>
<term>Hémangiosarcome ()</term>
<term>Hémangiosarcome (diagnostic)</term>
<term>Hémangiosarcome (mortalité)</term>
<term>Hémangiosarcome (étiologie)</term>
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<term>Taux de survie</term>
<term>Tumeurs du sein ()</term>
<term>Tumeurs du sein (mortalité)</term>
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<term>Lymphangiosarcoma</term>
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<front><div type="abstract" xml:lang="en">Stewart-Treves syndrome (SST) or former lymphangiosarcoma is a rare complication of chronic lymphoedema mainly related to the breast cancer (90% of cases). It occurs in 0.03% of patients surviving 10 or more years after radical mastectomy. The prognosis is very poor with a five-year survival close to 10% despite the various treatment modalities. The treatment of choice is a large resection, but some authors recommend radical resection in the form of shoulder disarticulation or forequarter amputation. Surgical treatment can be preceded or followed by radiation therapy. Locally advanced tumors or metastatic forms can be treated with mono or polychemotherapy, systemic or local.</div>
</front>
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